Fibrosarcomaa are rare malignant tumors arising in the deep soft tissues (muscles, ligaments, tendons, etc.). In children, fibrosarcomas are generally recorded under 5 years old, and in 10% cases they are congenital. The most typical tumor location is lower limbs, sometimes trunk, head and neck. Unlike adult fibrosarcomas, the childhood (infantile) fibrosarcomas almost do not form metastases and are characterized by a favorable prognosis. The ultimate diagnosis requires a biopsy.
The main treatment method is surgical removal of fibrosarcoma. The scope of interference depends on the size and location of the formation.
In most cases, it is possible to conduct a sparing surgery. The physician excises the maximum tumor volume, without disrupting the functions of the affected organ. For sarcomas of the lower extremities, the tumor is resected with the surrounding muscles, cartilage and bones affected by the tumor process. The bone graft or metal prosthesis is installed instead of the removed bone. After this intervention, the child needs an intensive rehabilitation course. The full recovery may take 3 to 12 months.
For severe injuries of extremities, if the tumor affected the important nerves and blood vessels, the amputation may be indicated. During surgery, the surgeon forms the cuff of the skin and muscles around the amputated bone, which facilitates the prosthesis installation. A temporary prosthesis is installed 10 to 14 days after the intervention, and a permanent one after 2 to 4 months, when the stump is healed completely.
In the event of an incomplete tumor removal or inoperable tumor, the radiotherapy is used. In children, the use of the modern techniques, which can significantly reduce the exposure of the growing healthy tissues is preferable. Depending on fibrosarcoma location, the following can be recommended:
- Radiosurgery (Cyber-Knife). The tumor is affected by a very high focused dose of radiation, which causes the death of cancer cells. The procedure is performed only once.
- Proton therapy. The tumor focus is irradiated with thin proton beams from different sides. The sessions are conducted on an outpatient basis for a few weeks.
Some patients with fibrosarcoma receive chemotherapy as an auxiliary method. Administration of anticancer drugs before surgery helps to reduce the tumor size and facilitate the implementation of surgical procedures, and to destroy the remaining cancer cells in the body after surgery and to avoid recurrence.Hide