Hematology: Hemophilia a b c — Diagnosis and symptomatic treatment. Treatment
Hemophilia is a hereditary pathology upon which there is a shortage of blood clotting factors. Depending on what factors are lacking, there are three versions of the disease, A, B and C. The leading symptoms of all varieties is the increased tendency to bleeding. Today, hemophilia cannot be cured completely, but its adequate therapy allows the patients to lead a full life.
Upon examination of the patient, the physician pays attention to the condition of his/her skin and mucous membranes. The information about previous bleedings is important. For final diagnosis, the patient is prescribed:
- complete blood count,
- blood chemistry
- abdominal ultrasound,
- integrated CT/MRI.
To establish the availability of a defective gene, the expert analyzes the genealogical data of the patient.
The main method of therapy is transfusions of the lacking blood factors performed upon acute hemorrhage or during remission as a preventive measure. For different types of the disease, the patients are administered the antihemophilic plasma, cryoprecipitate, PPSB and other drugs. The drug doses are selected on view of the patient’s age and weight.
Besides, the physician may recommend:
- antifibrinolytic drugs
- anti-inflammatory agents.
In each case, the set of therapeutic measures is chosen individually.Hide
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